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Wiskott Aldrich syndrome
Used for:
Aldrich syndrome
Used for:
Wiskott syndrome
Synonym for:
eczema thromocytopenia diarrhea syndrome
Synonym for:
eczema thromocytopenia immunodeficiency syndrome
Synonym for:
eczema thromocytopenia syndrome
Broader Terms:
congenital skin disorder
Broader Terms:
genetic disorder
Broader Terms:
inborn immunodeficiency
Broader Terms:
syndrome
Broader Terms:
thrombocytopenia
Related Terms:
sex linked trait
Scope Note:
rare x-linked immunodeficiency syndrome of young boys characterized by eczema, thrombocytopenic purpura and recurrent pyogenic infection; IGM levels are low and IGA and IGE levels are elevated; lymphoreticular malignancies are common.
Term Number:
1849-0285
Send your comments to: Melody Lowe