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Wiskott Aldrich syndrome

Used for:

Aldrich syndrome

Used for:

Wiskott syndrome

Synonym for:

eczema thromocytopenia diarrhea syndrome

Synonym for:

eczema thromocytopenia immunodeficiency syndrome

Synonym for:

eczema thromocytopenia syndrome

Broader Terms:

congenital skin disorder

Broader Terms:

genetic disorder

Broader Terms:

inborn immunodeficiency

Broader Terms:

syndrome

Broader Terms:

thrombocytopenia

Related Terms:

sex linked trait

Scope Note:

rare x-linked immunodeficiency syndrome of young boys characterized by eczema, thrombocytopenic purpura and recurrent pyogenic infection; IGM levels are low and IGA and IGE levels are elevated; lymphoreticular malignancies are common.

Term Number:

1849-0285


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