Prev Term: Taxus brevifolia
Next Term: TBI (traumatic brain injury)

Tay Sachs disease

Used for:

gangliosidosis GM2 type I

Used for:

hexosaminidase A deficiency

Broader Terms:

enzyme deficiency

Broader Terms:

gangliosidosis

Related Terms:

autosomal recessive trait

Scope Note:

autosomal recessive inherited gangliosidosis characterized by the onset in the first 6 months of life of an exaggerated startle response, delay in psychomotor development, hypotonia (followed by spasticity), visual loss, and a macular cherry red spot; hexosaminidase A is deficient, leading to the accumulation of GM2 ganglioside in neurons of the central nervous system and retina; this condition is strongly associated with Ashkenazic Jewish ancestry.

Term Number:

1849-8690


Send your comments to: Melody Lowe