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Refsum disease

Used for:

heredopathia atactica polyneuritiformis

Used for:

HMSN type IV

Used for:

phytanic acidemia

Broader Terms:

hereditary motor and sensory neuropathy

Broader Terms:

inborn lipid storage disorder

Related Terms:

autosomal recessive trait

Scope Note:

autosomal recessive disorder of lipid metabolism in which deficiency of phytanic acid alpha-hydroxylase results in accumulation of phytanic acid; manifested chiefly by chronic polyneuritis, retinitis pigmentosa, cerebellar ataxia and elevation of protein in cerebrospinal fluid.

Term Number:

2042-7949


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