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neuronal ceroid lipofuscinosis

Used for:

amaurotic familial idiocy

Used for:

Batten disease

Used for:

hereditary ceroid lipofuscinosis

Used for:

Kufs disease

Used for:

Vogt Spielmeyer disease

Broader Terms:

inborn lipid storage disorder

Broader Terms:

mental retardation

Scope Note:

inherited degenerative disease characterized by neuronal cytoplasmic inclusions which stain positively for ceroid and lipofuscin.

Term Number:

1849-6833


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