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Next Term: metachromatic leukoencephalopathy

metachromatic leukodystrophy

Used for:

arylsulfatase A deficiency

Used for:

metachromatic leukoencephalopathy

Used for:

metachromatic leukoencephaly

Used for:

sulfatide lipoidosis

Broader Terms:

enzyme deficiency

Broader Terms:

inborn lysosomal enzyme disorder

Broader Terms:

leukodystrophy

Related Terms:

autosomal recessive trait

Scope Note:

autosomal recessive lysosomal storage disease caused by a deficiency of cerebroside sulfatase leading to an accumulation of cerebroside sulfate in the nervous system and other organs.

Term Number:

1849-5593


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