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Menkes' syndrome

Used for:

kinky hair syndrome

Used for:

steely hair syndrome

Broader Terms:

cerebral degeneration

Broader Terms:

inborn metal metabolism disorder

Broader Terms:

syndrome

Related Terms:

sex linked trait

Scope Note:

X-linked recessive abnormality in copper absorption marked by severe cerebral degeneration and arterial changes resulting in death in infancy and by sparse, brittle scalp hair.

Term Number:

1849-5365


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