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kernicterus
Used for:
bilirubin encephalopathy
Broader Terms:
brain disorder
Broader Terms:
hyperbilirubinemia
Related Terms:
erythroblastosis fetalis
Related Terms:
perinatal blood group incompatibility
Scope Note:
brain disorder associated with high levels of bilrubin; clinical features include athetosis, muscle spasticity or hypotonia, impaired vertical gaze, and deafness; nonconjugated bilirubin enters the brain and acts as a neurotoxin, often in association with conditions that impair the blood-brain barrier; this condition occurs primarily in neonates with perinatal blood incompatibilities, but may rarely occur in adults.
Term Number:
1653-7303
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