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hereditary spherocytosis
Used for:
Minkowski Chauffard syndrome
Broader Terms:
congenital hemolytic anemia
Broader Terms:
genetic disorder
Related Terms:
autosomal dominant trait
Scope Note:
autosomal dominant trait marked by splenomegaly, jaundice, and fragile, spheroid erythrocytes which are prematurely cleared by the spleen; anemia is usually mild; treatment is splenectomy.
Term Number:
0427-1870
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