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congenital hepatic porphyria

Used for:

acute intermittent porphyria

Used for:

hereditary coproporphyria porphyria

Used for:

porphyria cutanea tarda

Used for:

porphyria intermittent acute

Broader Terms:

congenital disorder

Broader Terms:

liver disorder

Broader Terms:

porphyria

Scope Note:

disorders characterized by the liver excessively producing porphyrins or their precursors, arising from abnormalities in the regulation of the porphyrin-heme pathway existing at, and usually before, birth regardless of causation; porphyria, acute intermittent and porphyria cutanea tarda are types of hepatic porphyria.

Term Number:

1849-7674


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